Boccio Carlos M, Raffo Gabriela M Pérez, Parsini Cecilia
Hospital Italiano de Buenos Aires, ENT, Buenos Aires, Argentina.
Int J Pediatr Otorhinolaryngol. 2007 Nov;71(11):1803-7. doi: 10.1016/j.ijporl.2007.07.011. Epub 2007 Sep 6.
At the present time, the optimal management of patients with locally aggressive ELSTs includes: early diagnosis, surgical complete excision and long term follow up to monitor for recurrent disease. The presence of bilateral tumors produces a significant risk for bilateral profound hearing loss. We report the unusual case of bilateral endolymphatic sac tumor in a 14-year-old girl who presented bilateral anacusis and in whom a cochlear implant was performed after removal of the second tumor.
目前，对局部侵袭性内淋巴囊瘤患者的最佳治疗包括：早期诊断、手术完整切除以及长期随访以监测疾病复发。双侧肿瘤的存在会显著增加双侧严重听力丧失的风险。我们报告了一例罕见的14岁双侧内淋巴囊瘤女孩病例，该女孩出现双侧失聪，在切除第二个肿瘤后接受了人工耳蜗植入手术。
