多中心性恶性外周神经鞘瘤。

Multicentric malignant peripheral nerve sheath tumor.

作者信息

Ozturk Ersin, Erdem Iclal, Sonmez Guner, Haholu Aptullah, Sildiroglu Huseyin Onur, Mutlu Hakan, Basekim C Cinar, Kizilkaya Esref

机构信息

Department of Radiology, GATA Haydarpasa Teaching Hospital, Istanbul, Turkey.

出版信息

Clin Imaging. 2007 Sep-Oct;31(5):363-6. doi: 10.1016/j.clinimag.2007.04.028.

DOI:10.1016/j.clinimag.2007.04.028

PMID:17825749

Abstract

We present a case of malignant peripheral nerve sheath tumor of multicentric origin, an extremely rare condition. A 25-year-old man was admitted to hospital with presenting symptoms of cough, dyspnea and left lateral back pain. Computed tomography and magnetic resonance imaging revealed extrapleural masses in the left hemithorax in addition to synchronous left inguinal mass. After surgical resection of the masses from the thoracic and inguinal regions, histological examination confirmed the preoperative diagnosis of malignant peripheral nerve sheath tumor.

摘要

我们报告一例多中心起源的恶性外周神经鞘瘤，这是一种极为罕见的疾病。一名25岁男性因咳嗽、呼吸困难和左侧背部疼痛的症状入院。计算机断层扫描和磁共振成像显示，除了同步出现的左侧腹股沟肿块外，左半胸还有胸膜外肿块。在对胸部和腹股沟区域的肿块进行手术切除后，组织学检查证实了术前恶性外周神经鞘瘤的诊断。