Nishi T, Iwasaki M, Yamoto M, Nakano R
Department of Obstetrics and Gynecology, Arida City Hospital, Japan.
Acta Obstet Gynecol Scand. 1991;70(7-8):615-7. doi: 10.3109/00016349109007927.
Autosomal recessive polycystic kidney disease is a relatively rare congenital disease affecting the kidneys and liver. We noticed the kidney abnormality at 22 weeks gestation and observed the patient till the delivery at 36 weeks of gestation. The ultrasonographic features consisted of bilaterally enlarged hyperechogenic kidneys, oligohydramnios, lack of distention and difficulty in identifying the fetal urinary bladder. The serial sonographic features of the kidneys changed as pregnancy progressed. The kidney cysts gradually changed in size, shape and renal texture, but the umbilical velocimetry and the kidney circumference/abdominal circumference ratio did not change. Magnetic resonance imaging also showed similar characteristic features as observed by ultrasonography.
常染色体隐性多囊肾病是一种相对罕见的先天性疾病，会影响肾脏和肝脏。我们在妊娠22周时发现了肾脏异常，并对该患者进行观察直至妊娠36周分娩。超声特征包括双侧肾脏增大、回声增强、羊水过少、无扩张以及难以识别胎儿膀胱。随着妊娠进展，肾脏的系列超声特征发生了变化。肾囊肿在大小、形状和肾实质方面逐渐改变，但脐血流速度测定以及肾周长/腹围比值没有变化。磁共振成像也显示出与超声检查相似的特征。
