Bethge Wolfgang A, Faul Christoph, Bornhäuser Martin, Stuhler Gernot, Beelen Dietrich W, Lang Peter, Stelljes Matthias, Vogel Wichard, Hägele Matthias, Handgretinger Rupert, Kanz Lothar
Medical Center, University of Tübingen, Hematology/Oncology Otfried-Mueller Str. 1072076 Tuebingen, Germany.
Blood Cells Mol Dis. 2008 Jan-Feb;40(1):13-9. doi: 10.1016/j.bcmd.2007.07.001. Epub 2007 Sep 14.
Haploidentical hematopoietic cell transplantation (HHCT) after high dose conditioning with CD34-selected stem cells has been complicated by high regimen related toxicities, slow engraftment and delayed immune reconstitution leading to increased treatment related mortality (TRM). A new regimen using reduced intensity conditioning (RIC) and graft CD3/CD19 depletion with anti-CD3 and anti-CD19 coated microbeads on a CliniMACS device may allow HHCT with lower toxicity and faster engraftment. CD3/CD19 depleted grafts not only contain CD34+ stem cells but also CD34 negative progenitors, natural killer, graft facilitating and dendritic cells. RIC was performed with fludarabine (150-200 mg/m(2)), thiotepa (10 mg/kg), melphalan (120 mg/m(2)) and OKT-3 (5 mg/day, day -5 to +14) and no posttransplant immunosuppression. Twenty nine patients (median age=42 (range, 21-59) years) have been transplanted with this regimen. Diagnosis were AML (n=16), ALL (n=7), NHL (n=3), MM (n=2) and CML (n=1). Patients were "high risk" with refractory disease or relapse after preceding HCT. The CD3/CD19 depleted haploidentical grafts contained a median of 7.6x10(6) (range, 3.4-17x10(6)) CD34+ cells/kg, 4.4x10(4) (range, 0.006-44x10(4)) CD3+ T cells/kg and 7.2x10(7) (range, 0.02-37.3x10(7)) CD56+ cells/kg. Donor-recipient KIR-ligand-mismatch was found in 19 of 29 patients. The regimen was well tolerated with maximum acute toxicity being grade 2-3 mucositis. Because of severe neurotoxicity in 4 patients treated with 200 mg/m(2) fludarabine, the dose was reduced to 150 mg/m(2). Engraftment was rapid with a median time to >500 granulocytes/microL of 12 (range, 10-21) days, >20,000 platelets/microL of 11 (range, 7-38) days and full donor chimerism after 2-4 weeks in all patients. Incidence of grade II-IV degrees GVHD was 48% with grade II degrees =10, III degrees =2 and IV degrees =2. One patient, who received the highest T-cell dose, developed lethal grade IV GVHD. TRM in the first 100 days was 6/29 (20%) with deaths due to idiopathic pneumonia syndrome (n=1), mucormycosis (n=1), pneumonia (n=3) or GVHD (n=1). Overall survival is 9/29 patients (31%) with deaths due to infections (n=7), GVHD (n=1) and relapse (n=12) with a median follow-up of 241 days (range, 112-1271). In conclusion, this regimen is promising in high risk patients lacking a suitable donor, and a prospective phase I/II study is ongoing.
采用 CD34 选择的干细胞进行大剂量预处理后的单倍体相合造血细胞移植(HHCT),一直存在与方案相关的高毒性、植入缓慢和免疫重建延迟等问题,导致治疗相关死亡率(TRM)增加。一种新的方案采用减低剂量预处理(RIC),并在 CliniMACS 设备上使用抗 CD3 和抗 CD19 包被的微珠对移植物进行 CD3/CD19 清除,这可能使 HHCT 具有更低的毒性和更快的植入速度。CD3/CD19 清除的移植物不仅含有 CD34+干细胞,还含有 CD34 阴性祖细胞、自然杀伤细胞、移植物促进细胞和树突状细胞。采用氟达拉滨(150 - 200 mg/m²)、塞替派(10 mg/kg)、美法仑(120 mg/m²)和 OKT - 3(5 mg/天,第 -5 天至 +14 天)进行 RIC,且不进行移植后免疫抑制。29 例患者(中位年龄 = 42(范围 21 - 59)岁)接受了该方案移植。诊断包括急性髓系白血病(AML,n = 16)、急性淋巴细胞白血病(ALL,n = 7)、非霍奇金淋巴瘤(NHL,n = 3)、多发性骨髓瘤(MM,n = 2)和慢性粒细胞白血病(CML,n = 1)。患者均为先前造血干细胞移植(HCT)后难治性疾病或复发的“高危”患者。CD3/CD19 清除的单倍体相合移植物中,CD34+细胞中位数为 7.6×10⁶(范围 3.4 - 17×10⁶)个/kg,CD3+T 细胞中位数为 4.4×10⁴(范围 0.006 - 44×10⁴)个/kg,CD56+细胞中位数为 7.2×10⁷(范围 0.02 - 37.3×10⁷)个/kg。29 例患者中有 19 例供受者 KIR 配体不匹配。该方案耐受性良好,最大急性毒性为 2 - 3 级粘膜炎。由于 4 例接受 200 mg/m²氟达拉滨治疗的患者出现严重神经毒性,剂量减至 150 mg/m²。植入迅速,粒细胞>500/μL 的中位时间为 12(范围 10 - 21)天,血小板>20,000/μL 的中位时间为 11(范围 7 - 38)天,所有患者在 2 - 4 周后均达到完全供者嵌合。Ⅱ - Ⅳ度移植物抗宿主病(GVHD)的发生率为 48%,其中Ⅱ度 = 10 例,Ⅲ度 = 2 例,Ⅳ度 = 2 例。1 例接受最高 T 细胞剂量的患者发生致命性Ⅳ度 GVHD。前 100 天的 TRM 为 6/29(20%),死亡原因包括特发性肺炎综合征(n = 1)、毛霉菌病(n = 1)、肺炎(n = 3)或 GVHD(n = 1)。总体生存率为 9/29 例患者(31%),死亡原因包括感染(n = 7)、GVHD(n = 1)和复发(n = 12),中位随访时间为 241 天(范围 112 - 1271)。总之,该方案对于缺乏合适供者的高危患者很有前景,一项前瞻性Ⅰ/Ⅱ期研究正在进行。