Matsuda E, Okabe K, Matsuoka T, Hirazawa K, Azuma T, Murakami T, Sugi K
Department of Chest Surgery, National Hospital Organization Sanyo Hospital, Ube, Japan.
Kyobu Geka. 2007 Sep;60(10):950-3.
A 37-year-old man with von Recklinghausen's disease admitted to our hospital because of chest abnormal shadow. He had underwent extended radical tumorectomy for malignant peripheral nerve sheath tumor (MPNST) in left lower limb 33 months before. Chest X-ray and computed tomography (CT) scan revealed solitary tumor on right S10. Tumor was resected under thoracoscopic surgery. Histological diagnosis was metastasis of MPNST. MPNST with lung metastasis showing very poor prognosis. The patient is doing well 2 years after pulmonary resection without recurrence. Careful follow up is important for MPNST.
一名37岁患有冯雷克林霍增氏病的男性因胸部异常阴影入住我院。33个月前,他因左下肢恶性周围神经鞘瘤(MPNST)接受了扩大根治性肿瘤切除术。胸部X线和计算机断层扫描(CT)显示右S10有孤立性肿瘤。在胸腔镜手术下切除了肿瘤。组织学诊断为MPNST转移。MPNST伴肺转移预后极差。肺切除术后2年患者情况良好,无复发。对MPNST进行仔细随访很重要。