Kashiwagi Yasuyo, Kawashima Hisashi, Nishimata Shigeo, Nagao Ryuhei, Watanabe Kiyoko, Takekuma Kouji, Hoshika Akinori
Department of Pediatrics, Tokyo Medical University, Tokyo, Japan.
Clin Rheumatol. 2008 Feb;27(2):277-9. doi: 10.1007/s10067-007-0734-7. Epub 2007 Sep 22.
We describe a case of severe CINCA syndrome in a Japanese male infant. We recently managed with anti-interleukin 1 agent (anakinra). Anakinra immediately led to improvement of both the clinical symptoms and the laboratory findings.