Taniguchi Hisanori, Mishima Takao, Uchida Junji, Kinoshita Hidehumi
The Department of Urology, Saiseikai Izuo Hospital.
Hinyokika Kiyo. 2007 Sep;53(9):619-21.
A 64-year-old man who was diagnosed with type I neurofibromatosis was referred to our hospital with a pelvic mass incidentally found by ultrasonography. When examined by CT and MRI, the mass in the pelvis was 5 x 3 x 2 cm. In addition, another mass was found close to the obturator nerve at the S1-2 level. Transrectal biopsy was carried out, and a diagnosis of neurofibroma suspicious for low grade malignancy was made. We performed surgical resection of both of the tumors. The resected tumor was pathologically diagnosed as retroperitoneal malignant peripheral nerve sheath tumor (MPNST). We report our case and review the literature of MPNST detected in type I neurofibromatosis.
一名64岁男性，被诊断为I型神经纤维瘤病，因超声偶然发现盆腔肿物而转诊至我院。经CT和MRI检查，盆腔肿物大小为5×3×2 cm。此外，在S1-2水平靠近闭孔神经处发现另一个肿物。进行了经直肠活检，诊断为可疑低度恶性的神经纤维瘤。我们对这两个肿瘤均进行了手术切除。切除的肿瘤经病理诊断为腹膜后恶性外周神经鞘瘤（MPNST）。我们报告该病例并复习I型神经纤维瘤病中检测到的MPNST的文献。
Zotero 插件