Lanisnik Bostjan, Didanovic Vojko
Department for ENT-Head and Neck Surgery, Maribor General Hospital, Maribor, Slovenia.
Skull Base. 2007 May;17(3):211-4. doi: 10.1055/s-2007-977462.
To present the case of a rare tumor in the sphenoidoclival area and discuss potential pitfalls in diagnosis and management.
Case report with literature review.
Tertiary referral center.
Our patient presented with headache, vertigo, vision problems, and feeling of pressure in the central segment of the face. MR and CT showed a lesion in the body of the sphenoid, with signs of bone destruction and irregular borders. Differential diagnosis included intraosseous meningioma, chordoma, and inflammatory process.
Endoscopic/microscopic transnasal approach was performed to reach clival bone and to biopsy the tumor. Histopathological examination showed intraosseous lipoma.
Intraosseous lipoma is a rare tumor, or more accurately a hamartoma, and is usually found in the calcaneus or in the proximal femur. It is even rarer in the skull base. Usually it does not present any symptoms and is an incidental finding during imaging for other symptoms. As a rule it runs an indolent course and does not require any treatment. Since no definitive diagnosis can be made only on the basis of imaging (CT and MRI), it requires an open biopsy that if possible should be made in accordance with the principles of minimally invasive surgery.
介绍1例蝶枕区罕见肿瘤的病例,并探讨诊断和治疗中的潜在陷阱。
病例报告并进行文献复习。
三级转诊中心。
我们的患者出现头痛、眩晕、视力问题以及面部中央区域的压迫感。磁共振成像(MR)和计算机断层扫描(CT)显示蝶骨体有一个病变,伴有骨质破坏和边界不规则的迹象。鉴别诊断包括骨内脑膜瘤、脊索瘤和炎症过程。
采用内镜/显微镜下经鼻入路到达枕骨并对肿瘤进行活检。组织病理学检查显示为骨内脂肪瘤。
骨内脂肪瘤是一种罕见肿瘤,或者更准确地说是一种错构瘤,通常见于跟骨或股骨近端。在颅底更为罕见。通常它不表现出任何症状,而是在因其他症状进行影像学检查时偶然发现。通常它病程缓慢,不需要任何治疗。由于仅根据影像学检查(CT和MRI)无法做出明确诊断,因此需要进行开放性活检,且如果可能的话应按照微创手术原则进行。