Telem Dana A, Pertsemlidis David
The Mount Sinai Hospital, Department of Surgery, One Gustave Levy Plaza Box 1259, New York, NY 10029, USA.
J Gastrointest Surg. 2008 Sep;12(9):1609-11. doi: 10.1007/s11605-007-0395-5. Epub 2007 Nov 6.
Malignant peripheral nerve sheath tumors (MPNST) are defined as any tumor arising from a peripheral nerve or showing nerve sheath differentiation. The majority of these tumors arise on the trunk, extremities, or head and neck region. The literature to date has fewer than 14 cases of MPNST arising in the gastrointestinal tract, and only two cases were ever reported in the small intestine, one of which was a recurrent disease. In this paper, we report the first US case of an MPNST arising in the small intestine and presenting as intussusception.
恶性外周神经鞘瘤（MPNST）被定义为任何起源于外周神经或显示神经鞘分化的肿瘤。这些肿瘤大多数发生于躯干、四肢或头颈部区域。迄今为止的文献中，胃肠道发生的MPNST病例少于14例，小肠仅有两例报道，其中一例为复发性疾病。在本文中，我们报告了美国首例发生于小肠并表现为肠套叠的MPNST病例。
