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一例与Landau-Kleffner综合征相关的纯词聋:听觉障碍的长期研究

A case of pure word deafness associated with Landau-Kleffner syndrome: a long-term study of auditory disturbance.

作者信息

Notoya M, Suzuki S, Furukawa M, Enokido H

机构信息

ENT Department, School of Medicine, Kanazawa University, Japan.

出版信息

Auris Nasus Larynx. 1991;18(3):297-305. doi: 10.1016/s0385-8146(12)80266-5.

DOI:10.1016/s0385-8146(12)80266-5
PMID:1799334
Abstract

A long-term study of auditory disturbance of a female case who had suffered from pure word deafness associated with Landau-Kleffner syndrome was reported. The patient developed this syndrome at age 4, and we continued the follow-up until she reached 20. The following became clear after the investigation: (1) even by the age of 20 her auditory defect had not improved significantly; (2) from an early stage she could not identify either vowels or consonant-vowel syllables; (3) later she had no difficulty identifying vowels, but her consonant-discrimination score hardly improved; and (4) her problem in consonant identification was unique in that she could discriminate between the voiced and voiceless group but had great difficulty identifying the consonants within each group. These findings led to the conclusion that the patient is unable to recognize short time duration consonants due to an insensibility to loudness and a defect in temporal resolution.

摘要

报告了一例患有与Landau-Kleffner综合征相关的纯词聋女性患者听觉障碍的长期研究。该患者4岁时患上此综合征,我们持续随访至她20岁。调查后发现以下情况:(1) 即使到20岁,她的听觉缺陷仍未显著改善;(2) 从早期开始,她就无法识别元音或辅音-元音音节;(3) 后来她识别元音没有困难,但辅音辨别分数几乎没有提高;(4) 她在辅音识别方面的问题独特之处在于,她能区分浊音和清音组,但在识别每组内的辅音时存在很大困难。这些发现得出结论,该患者由于对响度不敏感和时间分辨率缺陷而无法识别短时长辅音。

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