Okuno Takashi, Oku Hidehiro, Kondo Mineo, Miyake Yozo, Sugasawa Jun, Utsumi Takashi, Ikeda Tsunehiko
Clin Exp Ophthalmol. 2007 Nov;35(8):781-3. doi: 10.1111/j.1442-9071.2007.01589.x.
Occult macular dystrophy (OMD) is an unusual inherited or sporadic macular dystrophy characterized by an essentially normal appearing ocular fundus and normal ocular circulation determined by fluorescein angiography but with a progressive decrease of visual acuity. We present a family with OMD who have a delay in the implicit times of both the visual-evoked potentials and the pupillary light reflexes. Because these delays are usually indicative of optic nerve disorders, deciding on a diagnosis between OMD and optic nerve disorder should be done carefully. We are not aware of any studies that have reported these findings in patients with OMD.
隐匿性黄斑营养不良(OMD)是一种罕见的遗传性或散发性黄斑营养不良,其特征是眼底外观基本正常,荧光素血管造影显示眼部循环正常,但视力逐渐下降。我们报告了一个患有OMD的家族,其视觉诱发电位和瞳孔光反射的潜伏时间均延迟。由于这些延迟通常提示视神经疾病,因此在OMD和视神经疾病之间做出诊断时应谨慎。我们不知道有任何研究报道过OMD患者的这些发现。