Nishida N, Takemoto T, Yamamoto C, Sugimoto T, Kuge M
Department of Pediatrics, Kansai Medical University, Otokoyama Hospital, Kyoto, Japan.
Acta Paediatr Jpn. 1991 Dec;33(6):714-7. doi: 10.1111/j.1442-200x.1991.tb02596.x.
Caroli's disease is a rare congenital anomaly of the liver. Since new diagnostic techniques for the evaluation of hepatic disease have been introduced, the number of reported cases of Caroli's disease has been gradually increasing. This report describes the case of a 13 year old girl with nausea, vomiting, fever and hepatomegaly. The diagnosis of Caroli's disease was established by ultrasonography and CT scan. The complications and management are discussed. The important points in management are to relieve symptoms and to conduct regular examinations by ultrasonography for the early detection of hepatobiliary carcinoma.
卡罗里病是一种罕见的肝脏先天性异常。自从引入了用于评估肝脏疾病的新诊断技术以来，卡罗里病的报告病例数一直在逐渐增加。本报告描述了一名13岁女孩出现恶心、呕吐、发热和肝肿大的病例。通过超声检查和CT扫描确诊为卡罗里病。文中讨论了其并发症及治疗方法。治疗的要点是缓解症状，并通过超声检查定期进行检查以便早期发现肝胆癌。
