Burgess N A, Lari J L
Department of Paediatric Surgery, University Hospital of Wales, Cardiff.
Br J Clin Pract. 1991 Autumn;45(3):223-4.
Pyoderma gangrenosum is an uncommon skin disorder characterised by deep ulcers surrounded by a violaceous over-hanging edge. Although in many instances there is no clear association with any underlying disease, pyoderma gangrenosum has been described in ulcerative colitis, Crohn's disease, polyarthritis, diabetes mellitus and myeloma. Pyoderma gangrenosum may also be seen as a rare manifestation of myeloproliferative disease including leukaemia. In children, as in our case, it may be the presenting feature.
坏疽性脓皮病是一种罕见的皮肤疾病,其特征为深部溃疡,周围有紫红色的悬垂边缘。尽管在许多情况下,它与任何潜在疾病都没有明确关联,但坏疽性脓皮病已在溃疡性结肠炎、克罗恩病、多关节炎、糖尿病和骨髓瘤中被描述过。坏疽性脓皮病也可能是包括白血病在内的骨髓增殖性疾病的一种罕见表现。在儿童中,就像我们这个病例一样,它可能是首发特征。