Ilyas Asif M, Nourissat Geoffroy, Jupiter Jesse B
Hand & Upper Extremity Service, Harvard Medical School, Massachusetts General Hospital, Boston, MA 02114, USA.
J Hand Surg Am. 2007 Dec;32(10):1538-42. doi: 10.1016/j.jhsa.2007.07.012.
A case of segmental neurofibromatosis of the upper extremity is presented. Multiple neurofibromas involving different peripheral nerves limited to a single body part or limb is a rare form of neurofibromatosis. The clinical, genetic, and histologic findings of segmental neurofibromatosis are described. The criteria for segmental neurofibromatosis are reviewed, and the differentiation of neurofibromatosis types 1 and 2 and schwannomatosis is also briefly reviewed.
