肝细胞癌、输血所致血色素沉着症和先天性再生低下性贫血（布莱克范-戴蒙德综合征）。
Hepatocellular carcinoma, transfusion-induced hemochromatosis and congenital hypoplastic anemia (Blackfan-Diamond syndrome).
作者信息
Steinherz P G, Canale V C, Miller D R
出版信息
Am J Med. 1976 Jun;60(7):1032-5. doi: 10.1016/0002-9343(76)90576-3.
PMID:180802
Abstract
A 25 year old patient with congenital hypoplastic anemia (Black-fan-Diamond syndrome) is described. This patient was hepatitis-antigen negative, had not received androgens and had a hepatoma develop in a transfusional hemochromatotic liver. Since androgens have been associated with hepatocellular carcinoma, the use of androgenic steroids for other than life-threatening symptoms in this disease should be avoided.
摘要
描述了一名25岁先天性再生障碍性贫血（布莱克-范-戴蒙德综合征）患者。该患者肝炎抗原阴性，未接受过雄激素治疗，在输血性血色素沉着症肝脏中发生了肝癌。由于雄激素与肝细胞癌有关，因此在这种疾病中，应避免在非危及生命的症状下使用雄激素类固醇。
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