Minotto Ivanete, Abdala Nitamar, Miachon Adriana Aparecida Siviero, Spinola e Castro Angela Maria, Imamura Paulo, Nogueira Roberto Gomes
Neuroradiology Ward, Image Diagnoses Department, Federal University of São Paulo, SP, Brazil.
Arq Neuropsiquiatr. 2007 Dec;65(4A):988-91. doi: 10.1590/s0004-282x2007000600013.
The basal encephaloceles refer to rare entities and they correspond to herniation of brain tissue through defects of skull along the cribiform plate or the sphenoid bone. A rare morning glory syndrome, with characteristic retinal defect has been reported in association with basal encephaloceles. Hypophysis hormonal deficiencies may occur. We accounted for a pituitary dwarfism with delayed diagnosed transsphenoidal encephalocele associated with morning glory syndrome, showing the alterations found in retinography, computed tomography and magnetic resonance imaging.
基底脑膨出是一种罕见的病症，它是指脑组织通过沿筛板或蝶骨的颅骨缺损处疝出。据报道，一种伴有特征性视网膜缺损的罕见牵牛花综合征与基底脑膨出有关。可能会出现垂体激素缺乏。我们报告了一例垂体性侏儒症，其经蝶骨脑膨出诊断延迟，与牵牛花综合征相关，并展示了视网膜造影、计算机断层扫描和磁共振成像中发现的改变。
