Bassarelli V, Baccetti T, Bassarelli T, Franchi L
Facoltà di Medicina e Chirurgia, Università degli Studi di Firenze.
Minerva Stomatol. 1991 Dec;40(12):811-9.
The authors describe the clinical and cephalometric characteristics of a case of Prader-Labhart-Willi syndrome (obesity, hypogonadism, oligophrenia, hypotonia, small hands and feet). Taurodontism and enamel-dentine dysplasia are reported as the main dental features. The craniofacial region shows an increased bony interorbital distance and a low level of the cribriform plate of the ethmoid bone. The possibility that these anomalies could be related to the etiopathogenesis of the syndrome is discussed.
