Treatment and outcome of intestinal failure secondary to enteric neuromuscular disease.

The clinical management of intestinal pseudoobstructive syndromes has, in the broadest of terms, 2 management strategies: optimisation of underlying gastrointestinal motor and absorptive function and, when this is inadequate, adequate nutritional support using enteral and intravenous nutrition to restore and maintain a good nutritional state and growth. With such support, a 10-year survival rate of >80% can be achieved in the most severely affected individuals without recourse to intestinal transplantation.