Ooi Masaya, Omoto T, Ishikawa N, Mouri M, Okayama T, Fukusumi M, Ono M, Tedoriya T
Department of Cardiovascular Surgery, Showa University, Tokyo, Japan.
Kyobu Geka. 2008 Jan;61(1):82-5.
Primary sarcoma of the pulmonary artery is rare. Diagnosis is difficult and often delayed; pulmonary embolism is part of the differential diagnosis. We treated a 46-year-old woman with progressive dyspnea. Computed tomography showed a lesion occupying the main pulmonary artery and peripheral branches on both sides. The pulmonary artery tumor, resected under cardiopulmonary bypass, was diagnosed pathologically as intimal sarcoma. Two weeks after the operation, the patient was feeling well and discharged from our hospital. Although the prognosis of pulmonary artery sarcoma is poor, early diagnosis and resection may prolong survival.
原发性肺动脉肉瘤罕见。诊断困难且常被延误;肺栓塞是鉴别诊断的一部分。我们治疗了一名46岁进行性呼吸困难的女性。计算机断层扫描显示一个病变占据双侧主肺动脉及外周分支。在体外循环下切除的肺动脉肿瘤经病理诊断为内膜肉瘤。术后两周,患者情况良好并出院。尽管肺动脉肉瘤预后较差,但早期诊断和切除可能延长生存期。