Bloomberg Richard D, Butany Jagdish W, Cusimano R J, Leask Richard L
Department of Pathology, Toronto General Hospital, University Health Network, Ontario, Canada.
Can J Cardiol. 2003 Jun;19(7):843-7.
Primary pulmonary artery neoplasms are rare and lethal. Those involving the pulmonary valve are even rarer with only a few reported cases in the literature. The poor prognosis of these neoplasms, despite attempted multimodal therapy, is largely related to delay and difficulty in diagnosis. The case of a 53-year-old woman is described who within one month of suddenly developing shortness of breath was found to have a mass arising from the pulmonary valve and extending through the pulmonary vasculature, requiring extensive surgical resection. She died two weeks postoperatively. The morphological findings of this primary pulmonary artery sarcoma are presented. Diagnosis, treatment, prognosis and literature are reviewed, and consideration of this tumour in the differential diagnosis of other pulmonary diseases is emphasized.
原发性肺动脉肿瘤罕见且致命。累及肺动脉瓣的肿瘤更为罕见，文献中仅有少数病例报道。尽管尝试了多模式治疗，但这些肿瘤预后不佳，主要与诊断延迟和困难有关。本文描述了一名53岁女性的病例，她在突然出现气短的一个月内，被发现有一个起源于肺动脉瓣并延伸至肺血管系统的肿块，需要进行广泛的手术切除。她在术后两周死亡。本文展示了该原发性肺动脉肉瘤的形态学表现。对诊断、治疗、预后及相关文献进行了综述，并强调在其他肺部疾病的鉴别诊断中应考虑到这种肿瘤。
