哈勒曼-施特雷夫综合征白内障手术后的渗出性视网膜脱离。

Exudative retinal detachment following cataract surgery in Hallermann-Streiff syndrome.

作者信息

Nishina Sachiko, Suzuki Yumi, Azuma Noriyuki

机构信息

Department of Ophthalmology, National Center for Child Health and Development, 2-10-1 Ohkura, Setagaya-ku, Tokyo 157-8535, Japan.

出版信息

Graefes Arch Clin Exp Ophthalmol. 2008 Mar;246(3):453-5. doi: 10.1007/s00417-007-0741-z. Epub 2008 Jan 12.

DOI:10.1007/s00417-007-0741-z

PMID:18193263

Abstract

PURPOSE

To report two cases of Hallermann-Streiff syndrome with exudative retinal detachment after cataract surgery.

METHODS

Case report.

RESULTS

Four eyes of two patients with Hallermann-Streiff syndrome developed exudative retinal detachments after lensectomy and anterior vitrectomy at 2 and 4 months of age. Both patients had extreme microphthalmia. The exudative retinal detachment regressed spontaneously in three of the four eyes; however, one eye required subscleral sclerectomy. In one patient, the best-corrected visual acuity was 20/200 at 3 years of age; the other patient had good fixation and following behavior in each eye at 1 year of age.

CONCLUSIONS

Early surgery to treat congenital cataracts in extremely microphthalmic eyes associated with the Hallermann-Streiff syndrome may induce exudative retinal detachment. However, the retinal detachments tend to regress and may not cause severe visual impairment.

摘要

目的

报告两例患有哈勒曼-施特雷夫综合征且在白内障手术后发生渗出性视网膜脱离的病例。

方法

病例报告。

结果

两名患有哈勒曼-施特雷夫综合征的患者的四只眼睛在2个月和4个月大时接受晶状体切除和前部玻璃体切除术后发生了渗出性视网膜脱离。两名患者均有极度小眼球症。四只眼睛中的三只眼睛的渗出性视网膜脱离自发消退；然而，一只眼睛需要进行巩膜下巩膜切除术。一名患者在3岁时最佳矫正视力为20/200；另一名患者在1岁时每只眼睛都有良好的注视和跟随行为。