Terzian Edward C, Schneider Ronald E
Long Island Jewish Medical Center, Department of Oral and Maxillofacial Surgery, Great Neck, NY 11040, USA.
J Oral Maxillofac Surg. 2008 Feb;66(2):349-54. doi: 10.1016/j.joms.2006.11.050.
Cystic fibrosis (CF) is now an adult disease. Approximately 30,000 children and adults are affected by this disease. CF, an autosomal recessive disease, is considered to be the most lethal inherited trait among Caucasians. The median age for the CF patient has significantly increased over the past 60 years. Today's oral and maxillofacial surgery practice is likely to include patients with CF with varying surgical needs. This article will review diagnosis, pathophysiology, and systemic complications of CF, and discuss relevant information for management of the CF patient for the oral and maxillofacial surgeon. Recommendations will be made for preoperative, perioperative, and postoperative care of these patients.
囊性纤维化（CF）如今已成为一种成人疾病。约3万名儿童和成人受此疾病影响。CF是一种常染色体隐性疾病，被认为是白种人中最致命的遗传性状。在过去60年里，CF患者的中位年龄显著增加。如今的口腔颌面外科业务中很可能会遇到有不同手术需求的CF患者。本文将回顾CF的诊断、病理生理学及全身并发症，并讨论口腔颌面外科医生在管理CF患者时的相关信息。将针对这些患者的术前、围手术期及术后护理提出建议。
