Woolf Kirsten M W, Wei Michael C, Link Michael P, Arber Daniel A, Warnke Roger A
Department of Pathology, Stanford University School of Medicine, Stanford, CA 94305-5324, USA.
Appl Immunohistochem Mol Morphol. 2008 Mar;16(2):196-201. doi: 10.1097/PAI.0b013e3180cc3211.
A 7-year-old boy presented with fulminant hepatic failure requiring liver transplant. Serologic testing ruled out infectious and autoimmune causes. During transplant surgery he was found to have enlarged periportal lymph nodes that were biopsied. Nodular lymphocyte-predominant Hodgkin lymphoma was diagnosed based on histologic examination of the lymph node and liver. The L&H cells within the lymph node were positive for CD20 whereas those within the liver were not, although they were positive for other B-cell markers. After extensive work-up, the cause of liver failure could only be attributed to the involvement by lymphoma. In addition, B-cell clonality was established among the neoplastic cells with the same clone detected in all sampled tissues. Hodgkin lymphoma as a cause of hepatic failure is rare and has not been previously reported in a pediatric patient.
一名7岁男孩出现暴发性肝衰竭,需要进行肝移植。血清学检测排除了感染性和自身免疫性病因。在移植手术过程中,发现他的肝门周围淋巴结肿大并进行了活检。根据淋巴结和肝脏的组织学检查,诊断为结节性淋巴细胞为主型霍奇金淋巴瘤。淋巴结内的L&H细胞CD20呈阳性,而肝脏内的L&H细胞CD20呈阴性,不过它们对其他B细胞标志物呈阳性。经过全面检查,肝衰竭的病因只能归因于淋巴瘤的累及。此外,在肿瘤细胞中确定了B细胞克隆性,且在所有采样组织中检测到相同的克隆。霍奇金淋巴瘤作为肝衰竭的病因较为罕见,此前尚未在儿科患者中报道过。