Shelton P A, Knopman D S
Section of Neurology, University of Manitoba, Winnipeg, Canada.
Arch Neurol. 1991 Jan;48(1):35-41. doi: 10.1001/archneur.1991.00530130043018.
The pattern of movement errors in ideomotor apraxia suggests an abnormality in selection and sequencing of component movements. Individuals with Huntington's disease were evaluated prospectively for the presence of apraxia, and aspects of motor and cognitive function were correlated with apraxic errors. Based on a conservative apraxia rating, ideomotor apraxia occurred in three (33%) of nine patients with a mean duration of disease of 10.4 years. Only two (22%) individuals made no apraxic errors, however, and the group as a whole made apraxic errors in 26% of movements. Apraxia was associated with errors in imitation of nonsymbolic movements but not with errors in recognition of gestures. It correlated significantly with duration of disease and with progressive abnormalities of posture but not with other individual aspects of elementary motor or cognitive function. These associations indicate that apraxia in Huntington's disease may be due primarily to involvement of subcortical motor structures rather than cerebral cortex.
观念运动性失用症中的运动错误模式表明在组成动作的选择和排序方面存在异常。对患有亨廷顿舞蹈症的个体进行前瞻性评估,以确定是否存在失用症,并将运动和认知功能方面与失用性错误相关联。基于保守的失用症评分,9名患者中有3名(33%)出现观念运动性失用症,平均病程为10.4年。然而,只有2名(22%)个体没有失用性错误,并且整个组在26%的动作中出现失用性错误。失用症与非象征性动作模仿中的错误相关,但与手势识别错误无关。它与病程以及姿势的进行性异常显著相关,但与基本运动或认知功能的其他个体方面无关。这些关联表明,亨廷顿舞蹈症中的失用症可能主要是由于皮质下运动结构而非大脑皮层受累所致。