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以持续性部分性癫痫为表现的副肿瘤综合征

[Paraneoplastic syndrome presenting as epilepsia partialis continua].

作者信息

Hâncu Anca

机构信息

Universitatea Ovidius Constanţa, Facultatea de Medicină, Spitalul Clinic de Urgenţă Constanţa, Clinica de Neurologie.

出版信息

Rev Med Chir Soc Med Nat Iasi. 2007 Jul-Sep;111(3):638-42.

Abstract

We describe a man of 59 years old, a smoker (20 cigarettes per day), without any pathologic background, with epilepsia partialis continua, with a relatively sudden appearance in the last 6 weeks. We wanted to find the cause of these prolonged focal seizures. The initial diagnosis of emergency was that of right side hemiballismus. The initial diagnosis on admission was prolonged right brachial myoclonus. Initially I was thinking of primary tumor or secondary one but paraclinic examinations excluded this diagnosis. After 5 months I repeated cerebral MRI scan which revealed left neoplasm of cavum. After another 6 months head and neck MRI described left rhinopharyngeal neoplasm with laterocervical adenopathies, cerebral metastases secondary to bronchopulmonary cancer with mediastinal invasion. The epilepsia partialis continua preceded by one year the primary neoplastic process.

摘要

我们描述了一名59岁男性,有吸烟史(每天20支),无任何病理背景,患有持续性部分性癫痫,在过去6周内相对突然出现。我们想找出这些持续性局灶性癫痫发作的原因。急诊的初步诊断为右侧偏身投掷症。入院时的初步诊断为持续性右侧臂肌阵挛。最初我考虑是原发性肿瘤或继发性肿瘤,但辅助检查排除了该诊断。5个月后,我再次进行脑部MRI扫描,结果显示左侧脑室囊肿。又过了6个月,头颈部MRI显示左侧鼻咽肿瘤伴颈侧淋巴结肿大,支气管肺癌继发脑转移并侵犯纵隔。持续性部分性癫痫发作比原发性肿瘤病程早一年出现。

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