School of Medicine, Hacettepe University, Ankara, Turkey.
Epileptic Disord. 2011 Mar;13(1):82-7. doi: 10.1684/epd.2011.0400.
Creutzfeldt-Jakob disease (CJD) is a rare form of rapidly progressive neurodegenerative disorder. Literature survey reveals only four reported cases of CJD with epilepsia partialis continua. Here, we present a review and a case study, with video-EEG sequences and characteristic MRI findings, of a fifth patient who presented with epilepsia partialis continua in the very early stage of the disease and followed a fatal course which was faster than expected. [Published with video sequences].
克雅氏病(CJD)是一种罕见的快速进展性神经退行性疾病。文献调查仅显示有四例伴有部分性癫痫持续状态的克雅氏病报告病例。在此,我们回顾性分析了第五例以疾病早期部分性癫痫持续状态起病并快速进展为特征的患者的临床、视频-脑电图(EEG)序列和磁共振成像(MRI)资料,并附有视频序列。[发表时有视频序列]