In vivo specific reduction of arylsulfatase B enzymatic activity in children with cystic fibrosis.

作者信息

Ferrero Giovanni Battista, Pagliardini Severo, Veljkovic Aleksandar, Porta Francesco, Bena Cristina, Tardivo Irene, Restagno Gabriella, Silengo Margherita Cirillo, Bignamini Elisabetta

出版信息

Mol Genet Metab. 2008 May;94(1):139. doi: 10.1016/j.ymgme.2007.10.010. Epub 2008 Mar 4.

DOI:10.1016/j.ymgme.2007.10.010

PMID:18299243

Abstract

摘要

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In vivo specific reduction of arylsulfatase B enzymatic activity in children with cystic fibrosis.

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