Erdogan Okan, Aksoy Alper, Turgut Nilda, Durusoy Elcim, Samsa Murat, Altun Armagan
Department of Cardiology, School of Medicine, Marmara University, Istanbul, Turkey.
J Electrocardiol. 2008 Jul-Aug;41(4):325-8. doi: 10.1016/j.jelectrocard.2008.02.023. Epub 2008 Mar 18.
Andersen-Tawil syndrome (ATS) is a rare, heterogeneous, autosomal dominant, or sporadic disorder characterized by the clinical triad of periodic paralysis, dysmorphic features, and ventricular arrhythmias such as bidirectional ventricular tachycardia (BVT). We present a case of an elderly patient with ATS whose symptomatic ventricular arrhythmias including BVT were effectively suppressed by oral verapamil therapy.
安德森-塔维尔综合征(ATS)是一种罕见的、异质性的常染色体显性或散发性疾病,其临床特征为周期性瘫痪、畸形特征以及室性心律失常,如双向性室性心动过速(BVT)。我们报告一例老年ATS患者,其包括BVT在内的有症状室性心律失常通过口服维拉帕米治疗得到有效抑制。