Srinivasan Jayasri, Leventer Richard J, Kornberg Andrew J, Dahl Henrik H, Ryan Monique M
Children's Neurosciences Centre, Royal Children's Hospital, Melbourne, Australia.
Pediatr Neurol. 2008 Apr;38(4):293-5. doi: 10.1016/j.pediatrneurol.2007.12.003.
The X-linked Charcot-Marie-Tooth disease is the second most common form of inherited neuropathy and, unlike most other forms of this disease, may present with atypical manifestations because of central nervous system involvement. Episodic central nervous system symptoms in X-linked Charcot-Marie-Tooth disease may be triggered by illness, dehydration, physical exercise, or exposure to altitude. We describe a child with transient episodes of hemiplegia after simple hyperventilation, a presentation not previously described in pediatric Charcot-Marie-Tooth disease type X.
X连锁型夏科-马里-图斯病是遗传性神经病的第二常见形式,与该疾病的大多数其他形式不同,由于中枢神经系统受累,可能会出现非典型表现。X连锁型夏科-马里-图斯病的发作性中枢神经系统症状可能由疾病、脱水、体育锻炼或暴露于高原引发。我们描述了一名儿童在简单的过度换气后出现短暂性偏瘫发作,这种表现以前在小儿X型夏科-马里-图斯病中未曾描述过。