丘疹性弹性组织离解，一种独特的病症？

Papular elastorrhexis, a distinctive entity?

作者信息

Del Pozo Jesús, Martínez Walter, Sacristán Felipe, Fernández-Jorge Beatriz, Fonseca Eduardo

机构信息

Department of Dermatology, Hospital Juan Canalejo, La Coruña, Spain.

出版信息

Am J Dermatopathol. 2008 Apr;30(2):188-90. doi: 10.1097/DAD.0b013e318164edb3.

DOI:10.1097/DAD.0b013e318164edb3

PMID:18360129

Abstract

Papular elastorrhexis is a rare entity of elastic tissue characterized by multiple white papules usually located on the trunk. We report a case of papular elastorrhexis in a 22-year-old man with sparse lesions and discuss the main controversial facts in this entity: its consideration as an independent disease or as an incomplete form of Buschke-Ollendorff syndrome and the confusion with and its possible inclusion as a variant of elastic tissue naevi.

摘要

丘疹性弹力纤维松解症是一种罕见的弹性组织疾病，其特征为多个白色丘疹，通常位于躯干。我们报告一例22岁男性的丘疹性弹力纤维松解症病例，其皮损稀疏，并讨论了该疾病主要存在争议的方面：它被视为一种独立疾病还是Buschke-Ollendorff综合征的不完全形式，以及与弹性组织痣的混淆及其可能作为弹性组织痣的一种变体被纳入其中。