Choonhakarn C, Jirarattanapochai K
Division of Dermatology, Department of Medicine, Faculty of Medicine, Srinagarind Hospital Medical School, Khon Kaen University, Thailand.
Clin Exp Dermatol. 2002 Sep;27(6):454-7. doi: 10.1046/j.1365-2230.2002.01051.x.
Papular elastorrhexis is a rare entity, possibly a form of multiple elastic tissue naevi. The cutaneous lesions in this disorder are characterized by multiple white papules usually occurring on the trunk. These tend to be nonfollicular and scattered evenly over the affected area. Histopathologically, there is a decrease of elastic fibres, that may also appear thin and fragmented. Most reported cases are sporadic but familial occurrence has been described and some authors believe that papular elastorrhexis may represent a mild form of Buschke-Ollendorff syndrome. We report an 18-year-old woman whose clinical and histopathological features were compatible with papular elastorrhexis. There was no evidence of skeletal changes or relevant family history.
丘疹性弹性组织离解是一种罕见的病症，可能是多种弹性组织痣的一种形式。该疾病的皮肤损害特征为通常出现在躯干上的多个白色丘疹。这些丘疹往往是非毛囊性的，在受累区域均匀分布。组织病理学上，弹性纤维减少，也可能显得纤细且破碎。大多数报道的病例为散发性，但也有家族性发病的描述，一些作者认为丘疹性弹性组织离解可能是布希克-奥伦多夫综合征的一种轻型表现。我们报告一例18岁女性，其临床和组织病理学特征符合丘疹性弹性组织离解。没有骨骼改变的证据或相关家族史。
