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类固醇诱导的骨纤维发育不良视力恢复

Steroid-induced visual recovery in fibrous dysplasia.

作者信息

Arroyo J G, Lessell S, Montgomery W W

机构信息

Department of Ophthalmology, Harvard Medical School, Boston, Massachusetts.

出版信息

J Clin Neuroophthalmol. 1991 Dec;11(4):259-61.

PMID:1838545
Abstract

Fibrous dysplasia is a rare disorder of bone that may be associated with acute loss of vision. Surgical intervention is generally advocated and sometimes restores vision in these patients. We report a case of a patient with unilateral optic neuropathy from fibrous dysplasia who suffered two acute episodes of visual impairment. The first episode of vision loss was reversed by surgery and the second by corticosteroid treatment. A trial of corticosteroid therapy may be beneficial in cases of acute vision loss due to fibrous dysplasia.

摘要

骨纤维异常增殖症是一种罕见的骨疾病,可能与急性视力丧失有关。通常提倡手术干预,有时手术可使这些患者恢复视力。我们报告一例因骨纤维异常增殖症导致单侧视神经病变的患者,该患者经历了两次急性视力损害发作。第一次视力丧失发作通过手术得以恢复,第二次则通过皮质类固醇治疗恢复。对于因骨纤维异常增殖症导致急性视力丧失的病例,试用皮质类固醇疗法可能有益。

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