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表现为“急性心肌梗死”的 Brugada 综合征

Brugada syndrome presenting as an "acute myocardial infarction".

作者信息

Gallahue Fiona E, Uzgiris Reda, Burke Ryan, Abrahams Wayne

机构信息

Department of Emergency Medicine, New York Methodist Hospital, Brooklyn, New York, USA.

出版信息

J Emerg Med. 2009 Jul;37(1):15-20. doi: 10.1016/j.jemermed.2007.09.038. Epub 2008 Apr 10.

DOI:10.1016/j.jemermed.2007.09.038
PMID:18403174
Abstract

Brugada syndrome is believed to be the cause of up to 50% of sudden cardiac death (SCD) cases due to ventricular dysrhythmias in young healthy individuals with no structural heart disease. This syndrome was first reported in 1992 and is rarely seen in the Emergency Department (ED). Given the life-threatening nature of Brugada syndrome, we hope to increase awareness in Emergency Medicine practitioners. We report the case of a 22-year-old man who was referred to the ED with a history of intermittent palpitations, near-syncope and electrocardiogram findings of RSR' and ST elevation in V1-V2 characteristic of Brugada syndrome. It is crucial that emergency physicians search for this diagnosis, as an implantable cardioverter-defibrillator is the only recognized life-saving intervention, and the risk of SCD is high if the diagnosis is missed.

摘要

在没有结构性心脏病的年轻健康个体中, Brugada综合征被认为是高达50%的因室性心律失常导致的心源性猝死(SCD)病例的病因。该综合征于1992年首次报道,在急诊科(ED)很少见。鉴于Brugada综合征危及生命的性质,我们希望提高急诊医学从业者的认识。我们报告了一例22岁男性病例,该患者因间歇性心悸、近乎晕厥的病史以及V1-V2导联出现RSR'和ST段抬高的心电图表现(这是Brugada综合征的特征)而被转诊至急诊科。急诊医生寻找这种诊断至关重要,因为植入式心脏复律除颤器是唯一被认可的救命干预措施,如果漏诊,SCD风险很高。

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