Hankinson Todd C, Ogden Alfred T, Canoll Peter, Garvin James H, Kazim Michael, Bruce Jeffrey N, Feldstein Neil A, Anderson Richard C E
Department of Neurosurgery, Columbia University, College of Physicians and Surgeons, New York, New York 10032, USA.
J Neurosurg Pediatr. 2008 May;1(5):389-91. doi: 10.3171/PED/2008/1/5/389.
Soft-tissue glomus tumors (or glomangiomas) are unrelated to neuroendocrine paragangliomas (glomus tympanicum, jugulare, and vagale). The authors present the first reported case of an orbital soft-tissue glomus tumor in a child. An 8-year-old girl developed rapidly progressive right-eye blindness, proptosis, and a sixth cranial nerve palsy. Magnetic resonance imaging demonstrated a homogeneously enhancing lesion extending from the right orbit through the superior orbital fissure to the cavernous sinus and middle cranial fossa. A biopsy specimen demonstrated the lesion to be a soft-tissue glomus tumor. Following angiography and embolization, a gross-total resection of the tumor was achieved. The patient was treated with adjuvant proton-beam radiotherapy. At 24 months follow-up her proptosis and sixth cranial nerve palsy had resolved and there was no evidence of tumor recurrence.
软组织血管球瘤（或血管球血管瘤）与神经内分泌副神经节瘤（鼓室球瘤、颈静脉球瘤和迷走神经球瘤）无关。作者报告了首例儿童眼眶软组织血管球瘤病例。一名8岁女孩出现右眼迅速进展性失明、眼球突出和第六脑神经麻痹。磁共振成像显示一个均匀强化的病变，从右眼眶经眶上裂延伸至海绵窦和中颅窝。活检标本显示该病变为软组织血管球瘤。在血管造影和栓塞治疗后，肿瘤实现了全切。患者接受了辅助质子束放疗。随访24个月时，她的眼球突出和第六脑神经麻痹已消退，且无肿瘤复发迹象。
