Baden W, Schaefer J, Kumpf M, Tzaribachev N, Pantalitschka T, Koitschev A, Ziemer G, Fuchs J, Hofbeck M
Dept of Paediatric Cardiology and Pulmology, Children's Hospital, University of Tuebingen, Hoppe-Seyler-Str. 1, D-72076 Tuebingen, Germany.
Eur Respir J. 2008 May;31(5):1125-31. doi: 10.1183/09031936.00045907.
Bridging bronchus (BB) is a rare, congenital bronchial anomaly that is frequently associated with congenital cardiac malformations, especially left pulmonary artery sling. It represents an anomalous bronchus to the right originating from the left main bronchus. Discrimination from other bronchial anomalies is important, since BB is frequently associated with bronchial stenoses due to abnormal cartilage rings. This case study describes the findings of bronchoscopy, bronchography and multidetector computed tomography (MDCT) in three patients. Bronchoscopy was helpful in the description of the severity and length of bronchial stenoses. However, it was not possible to establish a diagnosis of BB based on this method in two patients, since it is difficult or even impossible to differentiate the bifurcation from the pseudocarina. It was not possible to establish the correct diagnosis in all patients based on bronchography or MDCT. MDCT was able to depict the relationship of bronchial and vascular structures, which is particularly important in patients with pulmonary artery sling. Multidetector computed tomography is preferable to bronchography as it is less invasive and due to its short acquisition time it can be performed in children with severe respiratory disease. In the current authors' experience, detection of cartilage rings still requires flexible bronchoscopy.
桥接支气管(BB)是一种罕见的先天性支气管异常,常与先天性心脏畸形相关,尤其是左肺动脉吊带。它表现为起源于左主支气管的右位异常支气管。与其他支气管异常相鉴别很重要,因为BB常因软骨环异常而伴有支气管狭窄。本病例研究描述了3例患者的支气管镜检查、支气管造影和多排螺旋计算机断层扫描(MDCT)的结果。支气管镜检查有助于描述支气管狭窄的严重程度和长度。然而,在2例患者中,基于此方法无法确诊BB,因为很难甚至不可能将分叉与假隆突区分开来。基于支气管造影或MDCT也无法在所有患者中确诊。MDCT能够描绘支气管和血管结构的关系,这在患有肺动脉吊带的患者中尤为重要。多排螺旋计算机断层扫描优于支气管造影,因为它侵入性较小,且由于采集时间短,可在患有严重呼吸系统疾病的儿童中进行。根据作者目前的经验,软骨环的检测仍需要使用可弯曲支气管镜。