Medina-Escobedo G, Lopez-Corella E
Department of Pathology, Instituto Nacional de Pediatria, Mexico City, D.F.
Am J Med Genet. 1992 Oct 1;44(3):303-6. doi: 10.1002/ajmg.1320440308.
Sling left pulmonary artery (SLPA) is often associated with tracheobronchial abnormalities, including bridging bronchus (BB). We report on 3 patients with SLPA: One patient had a narrow trachea, absent right upper lobe and right main bronchus, and BB. The second patient had a long and narrow trachea, with normal segmentation of bronchial tree, abnormal cerebral gyri, and minor facial abnormalities. The third patient, with a normal trachea and main bronchi with BB, had imperforate anus, hemivertebrae, and atrial septal defect (VATER association). Patients with SLPA, those with BB, or those with both SLPA and BB as well as multiple congenital anomalies represent a spectrum of anomalies.
左肺动脉吊带(SLPA)常与气管支气管异常相关,包括桥接支气管(BB)。我们报告3例SLPA患者:1例患者气管狭窄,右上叶和右主支气管缺如,并有BB。第2例患者气管细长,支气管树分段正常,脑回异常,面部有轻微异常。第3例患者气管和主支气管正常但有BB,患有肛门闭锁、半椎体和房间隔缺损(VATER综合征)。SLPA患者、BB患者、同时患有SLPA和BB的患者以及有多种先天性异常的患者代表了一系列异常情况。