Sfaxi M, Bouzouita A, Bouasker I, Kourda N, Ben Slama M R, Ben Jilani Baltaji S, Chebil M
Service d'urologie, hôpital Charles-Nicolle, boulevard 9-Avril, 1006 Tunis, Tunisie.
Ann Endocrinol (Paris). 2008 Jun;69(3):249-53. doi: 10.1016/j.ando.2007.12.002. Epub 2008 May 1.
Primary adrenal lymphoma is a rare condition. Only 70 cases were described in the literature. Adrenal lymphoma is often bilateral and in most of the cases of B-cell type. T-cell lymphoma is exceptional. The prognosis is bad and patient can die early because of acute adrenal insufficiency. We report a case of a 70-year-old man who was admitted for acute adrenal insufficiency due to primary bilateral adrenal T-cell lymphoma. He had corticotherapy and surgical exploration for intra-abdominal sepsis. He died because of multivisceral deficiency. Clinical features and imaging are not specific. (18)F-FDG PET Scan is an excellent mean to detect malignant tumor of adrenal gland. Percutaneous needle biopsy is useful to determine histology. The standard treatment is chemotherapy.