Sfaxi M, Bouzouita A, Bouasker I, Kourda N, Ben Slama M R, Ben Jilani Baltaji S, Chebil M
Service d'urologie, hôpital Charles-Nicolle, boulevard 9-Avril, 1006 Tunis, Tunisie.
Ann Endocrinol (Paris). 2008 Jun;69(3):249-53. doi: 10.1016/j.ando.2007.12.002. Epub 2008 May 1.
Primary adrenal lymphoma is a rare condition. Only 70 cases were described in the literature. Adrenal lymphoma is often bilateral and in most of the cases of B-cell type. T-cell lymphoma is exceptional. The prognosis is bad and patient can die early because of acute adrenal insufficiency. We report a case of a 70-year-old man who was admitted for acute adrenal insufficiency due to primary bilateral adrenal T-cell lymphoma. He had corticotherapy and surgical exploration for intra-abdominal sepsis. He died because of multivisceral deficiency. Clinical features and imaging are not specific. (18)F-FDG PET Scan is an excellent mean to detect malignant tumor of adrenal gland. Percutaneous needle biopsy is useful to determine histology. The standard treatment is chemotherapy.
原发性肾上腺淋巴瘤是一种罕见疾病。文献中仅描述了70例。肾上腺淋巴瘤常为双侧性，且在大多数病例中为B细胞型。T细胞淋巴瘤较为罕见。预后较差，患者可能因急性肾上腺功能不全而早期死亡。我们报告一例70岁男性，因原发性双侧肾上腺T细胞淋巴瘤导致急性肾上腺功能不全入院。他接受了皮质激素治疗及针对腹腔内感染的手术探查。他因多脏器功能衰竭死亡。临床特征和影像学表现均不具有特异性。（18）F-FDG PET扫描是检测肾上腺恶性肿瘤的极佳手段。经皮穿刺活检有助于确定组织学类型。标准治疗方法是化疗。
