Erdol H, Kola M, Turk A, Akyol N
Department of Ophthalmology, Karadeniz Technical University, School of Medicine, Trabzon - Turkey.
Eur J Ophthalmol. 2008 May-Jun;18(3):479-82. doi: 10.1177/112067210801800331.
Posterior microphthalmos is a rare ocular abnormality. The authors report two siblings with bilateral posterior microphthalmos.
Two siblings (aged 10 and 13) were admitted with a history of low degree of vision. Ophthalmologic examinations, ocular ultrasonography, ultrasonic biomicroscopy (UBM), and optical coherence tomography (OCT) investigations were carried out and the results were evaluated. All results were also compared with their normal sibling.
Two siblings with posterior microphthalmos have normal and near normal anterior segment dimensions, shortened axial lengths (smaller than 17 mm), low vision with high hyperopias, papillomacular folds, and crowded optic discs. OCT investigation showed bilateral papillomacular retinal fold and UBM examination showed that ciliary body moved behind the iris towards the pupilla and the iridocorneal angle anomalies in two siblings. These findings were not observed in the normal sibling.
Posterior microphthalmos can exist in the presence of some ocular anomalies. In this case report, UBM provided new information about the structure of iridocorneal angle and ciliary body.
后部小眼球是一种罕见的眼部异常。作者报告了两名患有双侧后部小眼球的兄弟姐妹。
两名兄弟姐妹（年龄分别为10岁和13岁）因视力低下病史入院。进行了眼科检查、眼部超声检查、超声生物显微镜检查（UBM）和光学相干断层扫描（OCT）检查，并对结果进行了评估。所有结果还与他们正常的兄弟姐妹进行了比较。
两名患有后部小眼球的兄弟姐妹前节尺寸正常或接近正常，眼轴长度缩短（小于17毫米），高度远视导致视力低下，存在视乳头黄斑皱褶和拥挤的视盘。OCT检查显示双侧视乳头黄斑视网膜皱褶，UBM检查显示两名兄弟姐妹的睫状体向瞳孔方向移至虹膜后方且存在虹膜角膜角异常。这些发现在正常的兄弟姐妹中未观察到。
后部小眼球可能伴有一些眼部异常。在本病例报告中，UBM提供了有关虹膜角膜角和睫状体结构的新信息。
