无肝外胆管囊肿的I型胆道闭锁

Type I biliary atresia without extrahepatic biliary cyst.

作者信息

Komuro Hiroaki, Kudo Toyoichiro, Jinbo Takahiro, Hori Tetsuo, Tatekawa Yukihiro, Kudou Sumi, Urita Yasuhisa, Kaneko Michio

机构信息

Department of Paediatric Surgery, Institute of Clinical Medicine, University of Tsukuba, 1-1-1 Tennodai, Tsukuba, Ibaraki, Japan.

出版信息

Pediatr Radiol. 2008 Aug;38(8):907-8. doi: 10.1007/s00247-008-0871-4. Epub 2008 May 16.

DOI:10.1007/s00247-008-0871-4

PMID:18483732

Abstract

Currently, magnetic resonance cholangiography (MRC) is used for the differentiation of biliary atresia (BA) from other causes of infantile cholestasis. The authors present a case of type I BA without an extrahepatic biliary cyst in a 2-month-old girl. MRC clearly visualized the patency of the gallbladder, cystic duct, and hepatic ducts with disappearance of the common bile duct. Intraoperative cholangiography demonstrated a cloudy appearance of the intrahepatic bile ducts, confirming the diagnosis of type I BA. We believe that this is the first reported case of type I BA without an extrahepatic biliary cyst diagnosed by MRC.

摘要

目前，磁共振胆胰管造影（MRC）用于鉴别胆道闭锁（BA）与婴儿胆汁淤积的其他病因。作者报告了一例2个月大女童的I型BA，无肝外胆管囊肿。MRC清晰显示胆囊、胆囊管和肝管通畅，胆总管消失。术中胆管造影显示肝内胆管呈浑浊外观，证实为I型BA。我们认为这是首例通过MRC诊断的无肝外胆管囊肿的I型BA病例。