Benhammou A, Boulaadas M, Boulaich M, Benbouzid M A, Essakali L, Kzadri M
Service d'ORL et de chirurgie maxillofaciale, hôpital des spécialités, CHU de Rabat-Salé, Rabat, Maroc.
Rev Stomatol Chir Maxillofac. 2008 Jun;109(3):187-9. doi: 10.1016/j.stomax.2008.03.004. Epub 2008 May 27.
The retropharyngeal hematoma is rare and usually due to trauma, anticoagulation therapy complication or ascending aortic dissection. This presentation is extremely rare in hemophiliac patients.
A 23-year-old hemophiliac patient presented with a spontaneous onset large retropharyngeal hematoma extended to the floor of the mouth associated with dyspnea, dysphagia and dysphonia. The patient underwent adequate and successful medical treatment.
Hemophilia A is characterized by a deficit in factor VIII. Clinical symptoms are not specific and vary with the level of the intrinsic factor. Hematoma of the cervical region is a rare but potentially life-threatening event. The treatment requires transfusion of the specific factor and education of the patient and his relatives.
咽后血肿较为罕见,通常由外伤、抗凝治疗并发症或升主动脉夹层引起。这种情况在血友病患者中极为罕见。
一名23岁的血友病患者出现自发性巨大咽后血肿,血肿延伸至口腔底部,伴有呼吸困难、吞咽困难和声音嘶哑。该患者接受了充分且成功的药物治疗。
甲型血友病的特征是凝血因子VIII缺乏。临床症状不具特异性,且因内源性因子水平而异。颈部血肿虽罕见但可能危及生命。治疗需要输注特定因子,并对患者及其亲属进行教育。