Mackay Fabienne, Schneider Pascal
Autoimmunity Research Unit, The Garvan Institute of Medical Research, 384, Victoria Street, Darlinghurst, NSW 2010, Australia.
Cytokine Growth Factor Rev. 2008 Jun-Aug;19(3-4):263-76. doi: 10.1016/j.cytogfr.2008.04.006. Epub 2008 Jun 2.
BAFF is a B cell survival factor that binds to three receptors BAFF-R, TACI and BCMA. BAFF-R is the receptor triggering naïve B cell survival and maturation while BCMA supports the survival of plasma cells in the bone marrow. Excessive BAFF production leads to autoimmunity, presumably as the consequence of inappropriate survival of self-reactive B cells. The function of TACI has been more elusive with TACI(-/-) mice revealing two sides of this receptor, a positive one driving T cell-independent immune responses and a negative one down-regulating B cell activation and expansion. Recent work has revealed that the regulation of TACI expression is intimately linked to the activation of innate receptors on B cells and that TACI signalling in response to multimeric BAFF and APRIL provides positive signals to plasmablasts. How TACI negatively regulates B cells remains elusive but may involve an indirect control of BAFF levels. The discovery of TACI mutations associated with common variable immunodeficiency (CVID) in humans not only reinforces its important role for humoral responses but also suggests a more complex role than first anticipated from knockout animals. TACI is emerging as an unusual TNF receptor-like molecule with a sophisticated mode of action.
BAFF是一种B细胞存活因子,可与三种受体BAFF-R、TACI和BCMA结合。BAFF-R是触发初始B细胞存活和成熟的受体,而BCMA则支持骨髓中浆细胞的存活。BAFF产生过多会导致自身免疫,这可能是自身反应性B细胞不适当存活的结果。TACI的功能一直较为难以捉摸,TACI(-/-)小鼠揭示了该受体的两个方面,一个积极方面是驱动不依赖T细胞的免疫反应,一个消极方面是下调B细胞的活化和扩增。最近的研究表明,TACI表达的调节与B细胞上固有受体的活化密切相关,并且TACI对多聚体BAFF和APRIL的信号传导为浆母细胞提供了积极信号。TACI如何负向调节B细胞仍不清楚,但可能涉及对BAFF水平的间接控制。在人类中发现与常见可变免疫缺陷(CVID)相关的TACI突变,不仅强化了其在体液反应中的重要作用,也表明其作用比最初从基因敲除动物中预期的更为复杂。TACI正成为一种具有复杂作用模式的不同寻常的肿瘤坏死因子受体样分子。