Kollender Y, Shabat S, Nirkin A, Issakov J, Flusser G, Merimsky O, Meller I
The National Unit of Orthopedic Oncology The Tel-Aviv Sourasky Medical Center Tel Aviv Israel.
Sarcoma. 1999;3(2):85-8. doi: 10.1080/13577149977695.
Background. The origin of Ewing's sarcoma in a periosteal location is rare and not clearly documented. Other malignant bone tumors appear to have a somewhat better prognosis when confined between periosteum and bone. Is it the same for periosteal Ewing's sarcoma?Methods. We describe two new cases and comprehensively review the literature consisting of 18 documented cases since the condition was first described in 1986 (S.M. Bator.Cancer 58:1781- 4).Results. Periosteal Ewing's sarcoma differs from the other forms of Ewing's sarcoma in terms of sex predominance, location of tumor, surgical stage at presentation and typical imaging studies. Eighteen out of the 20 patients were reported to be alive with no evidence of disease.Conclusions. It seems that the prognosis of this rare variant of Ewing's sarcoma family of tumors might be better but the small number of cases precludes such a firm conclusion.
背景。尤因肉瘤起源于骨膜部位的情况较为罕见,且记录不明确。其他恶性骨肿瘤局限于骨膜与骨质之间时,预后似乎稍好一些。骨膜性尤因肉瘤的情况是否相同呢?
方法。我们描述了两例新病例,并全面回顾了自1986年首次描述该病症以来(S.M. 巴托尔。《癌症》58:1781 - 4)的18例已记录病例的文献。
结果。骨膜性尤因肉瘤在性别优势、肿瘤位置、初诊时的手术分期以及典型影像学检查方面与其他形式的尤因肉瘤不同。20例患者中有18例报告存活且无疾病证据。
结论。这种罕见的尤因肉瘤家族性肿瘤变体的预后似乎可能较好,但病例数量较少,无法得出如此确凿的结论。