Saint-Blancard P, Jancovici R
Service d'anatomie pathologique, hôpital d'instruction des Armées-Percy, B.P. 406, 101, avenue Henri-Barbusse, 92141 Clamart cedex, France.
Rev Med Interne. 2009 Feb;30(2):181-5. doi: 10.1016/j.revmed.2008.04.009. Epub 2008 Jun 6.
Solitary fibrous tumour is unusual, arising most commonly in the pleura and can also occur in a large number of other sites. We report the case of a 34-year-old man with a retroperitoneal solitary-fibrous tumour, revealed by abdominal pain and hypoglycaemia. We describe the histopathological and immunohistochemical features. Solitary-fibrous tumour should be included in the differential diagnosis of spindle cell tumours in this location. Despite complete local excision, local recurrence and metastasis are seen. The behaviour of theses tumours is unpredictable and patients with solitary fibrous tumour require careful and long-term follow-up.
孤立性纤维瘤较为罕见,最常发生于胸膜,也可出现在许多其他部位。我们报告一例34岁男性腹膜后孤立性纤维瘤病例,该病例因腹痛和低血糖而被发现。我们描述了其组织病理学和免疫组化特征。在该部位的梭形细胞瘤鉴别诊断中应考虑孤立性纤维瘤。尽管进行了完整的局部切除,但仍可见局部复发和转移。这些肿瘤的行为难以预测,孤立性纤维瘤患者需要仔细且长期的随访。