Iampol'skaia S A
Arkh Patol. 2008 Mar-Apr;70(2):48-50.
A case of a rare concomitance of airway scleroma and nonspecific aortoarteritis was studied in a 14-year-old girl, a native from the scleroma endemic Rovno Region. She had been treated for 4 years for this disease verified by a histological study of a laryngeal biopsy specimen. The fact that scleroma was a predictor of Takayasu's disease in this case cannot be ruled out; suggesting a pathogenetic association between both diseases. Concentric narrowing of the lumen of the aorta and its branching vessels contributed to the development of hypoxia and CNS ischemia, which worsened the severity of a pathological process in the airway and caused a fatal outcome during an episode of asphyxia.
对一名14岁女孩进行了研究,该女孩来自硬皮病流行的罗夫诺地区,患有罕见的气道硬结症与非特异性主动脉动脉炎并发的病例。通过对喉部活检标本的组织学研究确诊该病后,她接受了4年的治疗。不能排除在该病例中硬结症是高安氏病的一个预测指标;这表明两种疾病之间存在病因学关联。主动脉及其分支血管管腔的同心性狭窄导致缺氧和中枢神经系统缺血的发展,这加剧了气道病理过程的严重程度,并在一次窒息发作期间导致了致命后果。