Uehara Shuichiro, Oue Takaharu, Yoneda Akihiro, Hashii Yoshiko, Ohta Hideaki, Fukuzawa Masahiro
Department of Pediatric Surgery, Osaka University Graduate School of Medicine, 2-2 Yamadagaoka, Suita, Osaka, Japan.
Pediatr Surg Int. 2008 Aug;24(8):953-5. doi: 10.1007/s00383-008-2183-z. Epub 2008 Jun 10.
An 8-year-old boy was referred due to difficulty in walking. T1-weighted MRI detected a well-marginated lesion expanding from the epidural region in the spinal canal to the paravertebral area through the Th9 and Th10 intervertebral foramen. The patient underwent a biopsy under video-assisted thoracoscopy and the tumor was diagnosed as Ewing's sarcoma family of tumor (ESFT). Imaging confirmed that the tumor completely disappeared and his neurologic functions were recovered perfectly at the end of treatment. Very few cases of skeletal ESFT of epidural extension in childhood have been documented. Video-assisted thoracoscopic surgery remains the best option for the diagnosis of endothoracic tumors in children.
一名8岁男孩因行走困难前来就诊。T1加权磁共振成像(MRI)检测到一个边界清晰的病灶,从椎管内硬膜外区域经胸9和胸10椎间孔扩展至椎旁区域。该患者在电视辅助胸腔镜下进行了活检,肿瘤被诊断为尤因肉瘤家族性肿瘤(ESFT)。影像学检查证实肿瘤完全消失,治疗结束时其神经功能完全恢复。儿童期硬膜外扩展的骨骼ESFT病例记录极少。电视辅助胸腔镜手术仍然是诊断儿童胸内肿瘤的最佳选择。