Plastic and Maxillofacial Service, Ulster Hospital, Belfast BT16 1RH, Northern Ireland, UK.
J Plast Reconstr Aesthet Surg. 2009 Oct;62(10):e360-1. doi: 10.1016/j.bjps.2008.01.031. Epub 2008 Jun 20.
The aetiology of Poland syndrome remains unclear. It has been postulated that a developmentally normal foetus experiences a destructive process that subsequently results in cascading consequences eventually resulting in its characteristic features. We report the case of a male patient with Poland's anomaly who presented at birth with a large lymphangioma also affecting the right side of his chest. We propose that the pressure exerted by the space occupying lesion during embryological development lends further support to the existence of a subclavian artery supply disruption sequence as the causative insult.
波兰综合征的病因仍不清楚。据推测，一个发育正常的胎儿会经历一个破坏性的过程，随后会产生级联效应，最终导致其特征性表现。我们报告了一例男性波兰综合征患者，他出生时即患有巨大淋巴管瘤，也累及右侧胸部。我们提出，占位性病变在胚胎发育过程中产生的压力进一步支持了存在锁骨下动脉供应中断序列作为致病因素的假说。
