Gul Ahmet, Gedikbasi Ali, Oztarhan Kazim, Ceylan Yavuz
Maternal and Fetal Unit, Istanbul Bakirkoy Women's and Children's Hospital, Istanbul, Turkey.
J Ultrasound Med. 2008 Jul;27(7):1111-6. doi: 10.7863/jum.2008.27.7.1111.
Fetal echocardiography and color Doppler sonography have shown that most heart defects can be reliably diagnosed in utero by associated hemodynamic changes. Congenital ventriculocoronary fistulas associated with hypoplastic right heart syndrome (HRHS) and hypoplastic left heart syndrome (HLHS) have been described in the prenatal and neonatal periods, but little attention has been paid to their incidence and hemodynamic changes. There have been only a few reports of prenatal diagnosis of ventriculocoronary communications in HRHS and HLHS. Here we report prenatal diagnosis of HLHS and fistulas between the left ventricle and both the right and left coronary arteries to the pulmonary artery with a muscular ventricular septal defect (VSD) in a fetus at 23 weeks' gestation.
胎儿超声心动图和彩色多普勒超声检查表明，大多数心脏缺陷可通过相关的血流动力学变化在子宫内得到可靠诊断。先天性心室冠状动脉瘘与右心发育不全综合征（HRHS）和左心发育不全综合征（HLHS）相关，在产前和新生儿期已有描述，但对其发病率和血流动力学变化关注较少。关于HRHS和HLHS中心室冠状动脉交通的产前诊断仅有少数报道。在此，我们报告一例孕23周胎儿的HLHS以及左心室与左右冠状动脉至肺动脉之间的瘘合并肌部室间隔缺损（VSD）的产前诊断。
