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应激性心肌病作为长QT综合征和尖端扭转型室速的潜在病因。

Takotsubo cardiomyopathy as a potential cause of long QT syndrome and torsades de pointes.

作者信息

Ghosh Somnath, Apte Prachi, Maroz Natallia, Broor Apoorv, Zeineh Nabil, Khan Ijaz A

出版信息

Int J Cardiol. 2009 Aug 14;136(2):225-7. doi: 10.1016/j.ijcard.2008.04.021. Epub 2008 Jul 9.

DOI:10.1016/j.ijcard.2008.04.021
PMID:18617280
Abstract

Takotsubo cardiomyopathy is an increasingly reported syndrome characterized by transient apical left ventricular dysfunction in absence of flow limiting coronary artery disease. Prolongation of QT interval associated with Takotsubo cardiomyopathy has been previously reported in published case series but none of these series reported occurrence of torsades de pointes. Reported here is a case of Takotsubo cardiomyopathy resulting in QT prolongation and torsades de pointes in an emotionally distressed woman. The patient had a complete recovery of cardiac function in a week. Takotsubo cardiomyopathy should be considered among the causes of long QT syndrome and torsades de pointes.

摘要

应激性心肌病是一种报告日益增多的综合征,其特征为左心室心尖部短暂性功能障碍,而不存在冠状动脉血流受限性疾病。先前在已发表的病例系列中曾报告过与应激性心肌病相关的QT间期延长,但这些系列中均未报告有尖端扭转型室速的发生。本文报告了1例应激性心肌病导致1名情绪困扰女性出现QT间期延长及尖端扭转型室速的病例。该患者在1周内心脏功能完全恢复。应激性心肌病应被视为长QT综合征和尖端扭转型室速的病因之一。

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QT interval prolongation during ECG evolution in takotsubo cardiomyopathy poses a threat of torsade de pointes to predisposed patients. Case report of a female patient with congenital AV block.
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