Camargo da Silva Daniela Polo, Montovani Jair Cortez, Oliveira Danielle Tavares, Fioravanti Marisa Portes, Tamashiro Ivanira Ayako
Hospital das Clínicas, Faculdade de Medicina de Botucatu, Universidade do Estado de São Paulo.
Pro Fono. 2008 Apr-Jun;20(2):133-5. doi: 10.1590/s0104-56872008000200011.
the large vestibular aqueduct syndrome (LVAS) is characterized by the enlargement of the vestibular aqueduct associated with sensorioneural hearing loss. The level of hearing loss varies and may be fluctuant, progressive or sudden. Vestibular symptoms may be present. The diagnosis is reached by imaging methods.
To report an LVAS case.
a female infant was submitted to a computerized tomography of the ears and to audiologic tests.
enlargement of the vestibular aqueduct of more than 1.5mm and sensorioneural hearing loss in the right ear were observed.
with an early hearing evaluation it is possible to diagnose hearing loss, even in children were this loss is unilateral. Although the literature indicates that the diagnosis of LVAS occurs at a later age, in this case the etiologic diagnosis was enabled by computerized tomography.
大前庭导水管综合征(LVAS)的特征是前庭导水管扩大并伴有感音神经性听力损失。听力损失程度各异,可能呈波动性、进行性或突发性。可能存在前庭症状。通过影像学方法进行诊断。
报告一例大前庭导水管综合征病例。
对一名女婴进行耳部计算机断层扫描和听力测试。
观察到前庭导水管扩大超过1.5毫米,且右耳有感音神经性听力损失。
通过早期听力评估,即使是单侧听力损失的儿童也有可能诊断出听力损失。尽管文献表明大前庭导水管综合征的诊断多在较晚年龄做出,但在本病例中,通过计算机断层扫描实现了病因诊断。