Galati Vincenzo, Beeson James H, Confer Stephen D, Frimberger Dominic, Campbell Jeffrey B, Ramji Faridali G, Kropp Bradley P
Department of Urology, University of Oklahoma Health Sciences Center, 920 Stanton L. Young Boulevard, WP 3150, Oklahoma City, OK 73104, USA.
J Pediatr Urol. 2008 Apr;4(2):170-2. doi: 10.1016/j.jpurol.2007.04.003. Epub 2007 Jun 13.
Patients with severe prune belly syndrome rarely survive beyond the first days of life. We present a case of prune belly syndrome that initially presented with severe oligohydramnios, megacystis and associated poor urine biochemistries. Due to an anteriorly located placenta the patient was referred to three major centers, but was turned down because of the unfavorable prognostic findings. Therefore, fetal intervention was performed with 32 vesicocentesis and amnioinfusion procedures. Despite the unfavorable prenatal findings, and having undergone numerous fetal interventions, the birth resulted in a viable infant.